Autoimmune Inner Ear Disease (AIED) also known as Immune-mediated sensorineural hearing loss causes sensorineural hearing loss and vestibular symptoms. AIED occurs when the immune system attacks the cells within the inner ear. The body mistakes these cells for a virus or bacteria. It can be difficult to diagnosis because AIED can mimic various ear disorders.
SYMPTOMS OF THIS DISEASE
- Sudden hearing loss in one ear progressing rapidly to the second ear
- May feel fullness in the ear
- Experience vertigo
OUR DISEASE REPRESENTATIVES

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SPECIALISTS
- Otolaryngology Clinical Trial Cooperative Group (OCTCG)
- The American Academy of Otolaryngology Head and Neck Surgery Foundation
BLOOD TESTS
- Enthroycte Sedimentation Rate
- Rheumatoid Factor
- Anti-nuclear Antibody Titer
- Quantitative Immunoglobin Determination
- A Leukocyte Migration Inhibition Test
- Complete Blood Count
- FTS/ABS Blood Screen
- MRI
- Lymphocyte Blast Transformation
- Steroid Trial
- Liquid Panel
MEDICATIONS
- Steroids: dexamethasone, prednisone, and prednisolone
- Methotrexate: a chemotherapeutic agent
- Enbrel
- Imuran
TREATMENT
Most patients respond to the treatment of steroids. However, if patients are unresponsive to the drug therapy, a cochlear implant may be considered. In addition, some patients benefit from the use of hearing aids. |
AUTOIMMUNE RESOURCES
Here are some great websites, authors, podcasts and other resources to help you navigate your Autoimmune Disease.
AUTOIMMUNE STORIES
These are the women that have shared their autoimmune journey with us. Please take a moment to read some of their nrave, honest and revealing stories about their diagnosis, successes, hardships and their lives.